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KMID : 0383820090660050374
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Tuberculosis and Respiratory Diseases
2009 Volume.66 No. 5 p.374 ~ p.379
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A Case of Churg-Strauss Syndrome with Interstinal Perforation
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Park Jeong-Hoon
Kim Yang-Ki
Lee Young-Mok
Kim Ki-Up
Uh Soo-Taek
Kim Jae-Joon
Jung Yun-Seok
Hwang Jeong-Hwa
Kim Dong-Won
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Abstract
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Churg-Strauss syndrome (CSS) or allergic granulomatous angiitis is a rare syndrome that is characterized by hypereosinophilic systemic necrotizing vasculitis affecting small- to medium-sized arteries and veins. In general, it occurs in individuals with pre-existing allergic asthma. When CSS appears in patients, it has the following characteristics: eosinophilia of more than 10% in peripheral blood, paranasal sinusitis, pulmonary infiltrates, histological proof of vasculitis with extravascular eosinophils, and mononeuritis multiplex or polyneuropathy. Therapeutic trials dedicated to Churg-Strauss syndrome have been limited due to the rarity of this disorder and the difficulty in making a histological diagnosis. Proper treatment of patients with CSS is not widely known. In this case study, we report on our experience with an unusual patient case, characterized by purpura and a perforation of the small intestine after inadequate steroid therapy.
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KEYWORD
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Churg-Strauss syndrome, Asthma, Intestinal perforation, Eosinophilic infiltration.
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